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Description

Secretion of glucagon is stimulated by: Hypoglycemia Epinephrine (via 2, 2, [14] and 1 [15] adrenergic receptors) Arginine Alanine (often from muscle-derived pyruvate/glutamate transamination (see alanine transaminase reaction)

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Huo, Y.-X

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Our patient was diagnosed with severe GSSD after neonatal onset, with symptoms including hemolytic anemia, hyperbilirubinemia and severe metabolic acidosis (intractable), urine-organic acid analysis results suggestive of the presence of 5-oxoprolinuria, and imaging results suggestive of central nervous system damage and developmental retardation in the infant at follow-up

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Ann Acad Med Singapore

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